These tumours are locally aggressive, meaning they can grow and invade nearby tissues but do not metastasise to other parts of the body. They can occur in various locations, including the abdominal wall, the intra-abdominal region, the extremities and other soft tissue areas, and are categorised as intermediate-grade tumours between benign and malignant due to their invasive nature.
Symptoms can vary depending on the location and size of the tumour, and may include a palpable mass, pain, limited range of motion and compression of nearby structures.
Treatment depends on several factors, such as the size and location of the tumour, symptoms and individual patient considerations. It may include observation with regular monitoring, surgery, radiation therapy, targeted therapy or systemic therapy. A multidisciplinary approach involving oncologists, surgeons and other healthcare professionals is often used. Because of its locally aggressive nature, ongoing monitoring and follow-up care are important to detect any recurrence or progression.
No subtypes found.
